Surgical repair in coexisting transposition of the great arteries with infracardiac obstructed total anomalous pulmonary venous connection

Coexisting transposition of the great arteries (d-TGA) and total anomalous pulmonary venous connection (TAPVC) is a rare combination, with the infracardiac variety being more rare. So far, only a few cases are described in the literature with combined infracardiac TAPVC and d-TGA. We present a 4-month-old girl having TGA and obstructed infracardiac TAPVC with early left ventricle mass regression. She underwent successful complete surgical anatomical correction of this rare entity without postoperative mechanical circulatory support uneventfully. Simultaneous complete anatomical correction of TAPVC and d-TGA with arterial switch operation and common chamber to left atrium anastomosis can be done with excellent outcome even in late presentation with features of obstruction.