DOI: 10.1111/cen.70190 ISSN: 0300-0664

Self‐Reported Health Burden and Quality‐of‐Life–Related Concerns in Patients With Achondroplasia: A Survey From Türkiye

Zehra Aycan, Murat Berge, Sukran Darcan, Saadet Olcay Evliyaoglu, Fatih Suheyl Ezgu, Ercan Mihci, Feristah Ferda Ozkinay

ABSTRACT

Objective

Achondroplasia is an autosomal dominant genetic disorder, characterised by distinctive growth patterns and recognisable skeletal features. This study aimed to determine the demographic and clinical characteristics, quality of life (QoL) losses, and expectations of individuals with achondroplasia in Türkiye.

Design

In this survey‐based study, Computer‐Assisted Telephone Interviewing (CATI) system was used and questions were directed to patients or their parents via phone calls.

Patients

A total of 140 patients with achondroplasia, of whom 50.7% were male (age range, 0–20 years) were included.

Measurements

The questionnaire forms were prepared by a committee including clinicians and the president of the Achondroplasia and Families Association. The forms included questions on sociodemographic characteristics, diagnosis and treatment, expectations from the patient association, and quality of life.

Results

Achondroplasia was commonly diagnosed by obstetricians (76.5%) and the patients were followed by multiple specialties. Of the patients, 10% received growth hormone treatment, and 55.7% underwent at least one surgical procedure, with 23.6% undergoing limb lengthening surgery. The main symptoms frequently/very frequently observed in the patients were: sleep‐disordered breathing (40%), recurrent ear infections (32%), and frequent respiratory tract infections (28%). The primary concerns involved experiences of social exclusion due to physical appearance and together with related psychological challenges. The main expectations of the participants and parents from the association were to receive education on achondroplasia management and new treatment options, and to promote public awareness.

Conclusions

Patients with achondroplasia face significant challenges in daily life, they require medical treatment and some supportive services to improve their quality of life.

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