DOI: 10.4103/jpgm.jpgm_194_26 ISSN: 0022-3859

POEMS syndrome with atypical presentation: A rare case

S Singhal, MM Bharath, R Verma, VK Paliwal

ABSTRACT

POEMS is an uncommon paraneoplastic plasma cell disorder known with the expansion of polyneuropathy, organomegaly, endocrine abnormalities, M-band, and skin changes. We report a patient presenting with monoarthritis and weight loss for 5 months, who was treated empirically for tuberculous arthritis and later developed debilitating axonal polyneuropathy due to delayed diagnosis. POEMS/Plasma cell dyscrasias rarely involve joints, and this case highlights this unique presentation of POEMS syndrome. Bone biopsy from the affected joint revealed the diagnosis. Chronic large-joint monoarthritis with systemic symptoms, mimicking tuberculous arthritis, and polyneuropathy is a unique combination—so clinicians should consider an underlying plasma cell dyscrasia/POEMS to avoid delayed diagnosis.

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