DOI: 10.1002/rcr2.70721 ISSN: 2051-3380

Cystic Lung Changes in Inclusion Body Myositis: An Unusual Pulmonary Manifestation

Gehad Othman, Thasniya Ummer, Heshani De Silva, Harshana Bandara, Hector Chinoy

ABSTRACT

Idiopathic inflammatory myopathies (IIMs) are chronic autoimmune disorders affecting skeletal muscles, with pulmonary involvement in 30%–40% of cases. Inclusion body myositis (IBM) is a distinct subset that usually does not involve the lungs. This report highlights a rare case of inclusion body myositis presenting with pulmonary disease.

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