DOI: 10.1002/ccr3.73010 ISSN: 2050-0904

Congenital Atrophic Dermatofibrosarcoma Protuberans: A Case Report and Narrative Review of the Literature

Sima Shamshiri Khamene, Izat Mohammad Khawajah, Taha Shahbazi, Safoura Shakoei

ABSTRACT

Dermatofibrosarcoma protuberans is a rare dermal and subcutaneous soft‐tissue tumor, uncommon in children, characterized by CD34 positivity and COL1A1‐PDGFB fusion. Prognosis is generally good, but local recurrence risk is high, so complete excision with clear margins and six‐monthly follow‐up for three years after surgery is recommended in most cases.

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