DOI: 10.1093/ced/llag354 ISSN: 0307-6938
Confusion, Rash and a Rapid Deterioration
Alistair Ludley, Yasmin Khan, Parastoo BabakinejadA 72-year-old man presented with a violaceous rash, confusion and profound hyperferritinaemia, later diagnosed as anti-MDA5 dermatomyositis. His course was rapidly progressive and complicated by encephalopathy and spontaneous retroperitoneal haemorrhage, reflecting a severe hyperinflammatory phenotype. This case underscores the importance of early recognition of this often fulminant form of dermatomyositis to improve outcomes.