A RARE CASE OF PLEURO-SCLERODERMA

Scleroderma or systemic sclerosis (SSc) is an inammatory- brotic disease that results in deposition of excessive extracellular matrix in the skin and several visceral organs including the lungs, heart, kidneys, and gastrointestinal tract(1). Pulmonary complications of SSc remain one of the largest causes of morbidity and mortality in the disease. Interstitial lung disease (ILD) and pulmonary arterial hypertension (PAH) are the most common forms of lung manifestation associated with SSc(2).