DOI: 10.4103/iju.iju_340_23 ISSN: 0970-1591
Metastatic alveolar soft part sarcoma of the kidney in a young female
Shritosh Kumar, Brusabhanu Nayak, Vandna Bharati, Seema Kaushal, Mehar Chand Sharma- Urology
ABSTRACT
A 19-year-old female presented with left flank discomfort and swelling. Imaging revealed a large mass arising from the left kidney, and radical nephrectomy confirmed the diagnosis of alveolar soft part sarcoma (ASPS) based on histopathological and ultrastructural examination. Postoperatively, positron emission tomography–computerized tomography showed lung metastasis and renal bed recurrence. Sunitinib was initiated for metastatic ASPS. This case underscores challenges in diagnosing and managing ASPS, highlighting the role of tyrosine kinase inhibitors. Multidisciplinary care and vigilant follow-up are crucial for rare tumors such as ASPS.